Porphyria disease is a rare hemoglobin disorder which is said to be caused due to hereditary factors. It is considered a hereditary disease which states abnormal metabolism of the blood pigment hemoglobin.
What is Porphyria?
The term Porphyria refers to a group of eight different disorders described by the accumulation of porphyrins or porphyrin precursors in the body. Porphyrins are necessary for the function of hemoglobin – a protein in the red blood cells that links to porphyrin, binds iron and carries oxygen to your organs and tissue.
Porphyria is rare. Doctors don’t know the exact number of people living with this condition because numerous have no symptoms of the disease.Porphyria can affect the nervous system or skin. Sometimes both are affected. The condition may or may not cause symptoms. Symptoms may develop over hours or days and last for days or weeks.
Under normal conditions porphyrins are made by the body in small amounts during the synthesis of heme. Heme is a necessary element of hemoglobin which is responsible for transporting oxygen through our bodies. It is produced in a sequence of chemical reactions each one under the control of an exact enzyme. If one of these enzymes is defective there is a buildup of porphyrins or their precursors which may accumulate to toxic levels. Each porphyria is caused by shortage of a particular enzyme in the pathway.
Treatment depends on the kind of porphyria you have and the severity of symptoms. Treatment includes identifying and avoiding symptom triggers and then dismissing symptoms when they occur. Herbal Treatment for Porphyria is better solution for reducing the symptoms.
Key Facts of Porphyria
- Porphyria disease mainly affect skin or the nervous system that can cause pain in the abdomen.
- It is an inherited disorder caused due to gene abnormalities.
- Cells in patients suffering from Porphyria disease fail to change body chemicals known as porphyrins.
- In this disorder porphyrins become dark and the blood loses its fresh red color.
- This disorder usually leads to mental disturbances and increase skin sensitivity to light.
- Porphyrins and porphyrin precursors of heme when start building up in the human body they give way to this disorder.
- There are two common types of Porphyria which include:
Acute porphyrias which normall have an impact on the nervous system. They last for a short period of time
Cutaneous porphyrias which have a direct impact on the skin.
- The exact occurrence rate of this disorder varies all around the globe.
- It is identified with blood, urine and usually stool tests.
- In extreme cases where the onset of disease is severe a health care professional usually recommend liver transplantation.
- It is caused due to certain enzyme deficiencies.
Causes of Porphyria
There is a lineup of Causes of Porphyria that have been recognized which are believed to be responsible for causing this disorder. In cutaneous porphyria the porphyrins grow in the skin and when exposed to sunlight cause symptoms. In acute porphyria, the buildup damages the nervous system.
There are listed here for Causes of Porphyria:
- Consuming too much iron
- All kinds of stress
- Crash dieting or fasting
- Excessive use of alcohol or estrogen.
- Excessive smoking
- A long lasting liver disease such as chronic hepatitis C
- HIV virus responsible for causing AIDS
- Gene abnormalities linked with hemochromatosis which caused buildup of iron in the body
- Regular use of some medications or hormones
- Excessive exposure to sunlight
Symptoms of Porphyria
Symptoms of Porphyria do not commonly appear until well after puberty and are seen more in women than in men and more likely to happen during menstruation. The majority of people who inherit the condition do not have attacks. Where symptoms do take place, they are sudden and can last for days or weeks.
Porphyria causes three major Symptoms of Porphyria:
- Abdominal pain or cramping
- Problems with the nervous system and muscles
- Sensitivity to light that can cause rashes, blistering and scarring of the skin
There are some key Symptoms of Porphyria that make it easier for the health care professionals to recognize this disorder before they can go onto beginning the high-end disease management routine.
Here’s a compiled list of symptoms for reference:
Attacks of acute porphyria may unfold or progress with the following Symptoms of Porphyria:
- Anxiety, restlessness and insomnia
- Severe abdominal pain
- Reddish coloured urine
- Pain in your arms, legs or back
- Vomiting and constipation
- High blood pressure
- Confusion, hallucinations and seizures
- Muscle pain, tingling, numbness, weakness or paralysis
- Breathing difficulties possibly requiring ventilation
Porphyria can cause Symptoms of Porphyria that affect the nervous system. These symptoms mostly occur suddenly and generally last a short period of time.
Diagnosis of Porphyria
Porphyria is diagnosed through blood, urine, and stool tests, especially at or near the time of symptoms. Diagnosis of Porphyria may be difficult because the range of symptoms is common to various disorders and interpretation of the tests may be difficult. A large number of tests are accessible however but outcomes among laboratories are not always reliable.
Diagnosis of Porphyria is difficult because most symptoms are non-specific for example abdominal pain and can often be caused by many further conditions. Even for people with porphyria it is possible that indications can be caused by other underlying problems.
Prognosis of Porphyria
The Prognosis of Porphyria usually good if the disease is recognized and if treatment is prompt before severe nerve develops. Even though symptoms commonly resolve after an attack, repair of nerve damage and connected muscle weakness may require some months or longer. Mental symptoms may take place during attacks but are not chronic. Premenstrual attacks often resolve rapidly with the onset of menses.
Risk Factors of Porphyria
Caucasians are at greater Risk Factors of Porphyria. Women are also at increased risk because porphyria is connected to the menstrual cycle. The most common risk of porphyria is having a family member with the disease.
Porphyria attacks may be triggered by:
- Dieting or fasting
- Physical stress for example infections or other illnesses
- Liver disease
- Emotional stress
- Alcohol use
- Menstrual hormones
- Sun exposure
- Excess iron in your body
Complications of Porphyria
Possible Complications of Porphyria include:
- Vomiting due to an attack of acute porphyria can lead to dehydration, which may need that you receive fluids through a vein
- Called hyponatremia, this is generally connected to problems with sodium and water handling in your body
- Porphyrin buildup can damage your kidneys and may effect in high blood pressure
- Porphyrin buildup may cause your kidneys to slowly lose their ability to function
- Acute porphyria can cause muscle weakness and paralysis which can cause breathing problems. If left untreated they can also lead to respiratory failure
Key Points of Porphyria
Key Points of Porphyria include are:
- Attacks have many triggers, including hormones, drugs, low-calorie and low-carbohydrate diets, and alcohol ingestion
- Treat acute attacks with oral or IV dextrose and for severe attacks, IV heme
- Urine is often reddish-brown during an attack
- Do a qualitative urine test for porphobilinogen and confirm a positive result with quantitative delta-aminolevulinic acid and PBG measurements
Prevention of Porphyria
Most types of porphyria are inherited and can therefore not be Prevention of Porphyria. Risks vary depending on the type but about half can happen if one altered gene is passed from one parent.
Carriers of porphyria should avoid the following:
- Crash diets
- Potentially harmful drugs
- Heavy alcohol utilize
- Physical or emotional stress or exhaustion
- Periods of starvation
- Exposure to organic solvents eg, in painting or dry cleaning
Herbal Treatment for Porphyria
There is no long-term cure for this condition. Natural Herbal Treatment for Porphyria can be used safely and effectively in the management of porphyria. The porphyria symptoms are interpreted in the light of natural herbal way and treated accordingly.
Natural Herbs are a very simple and inexpensive Herbal Treatment for Porphyria. The anti-inflammatory and antioxidant properties of natural herbs is very beneficial in the treatment of various disorders. Different herbs can also be combined with several other herbs for better results.
In herbal treatment such symptoms correspond to the disease appears mainly due to a combine dysfunction of natural herbs and herbal supplement. Herbal Treatment for Porphyria is therefore aimed at treating causes dysfunction and reducing symptoms.
There is another excellent herb used for the herbal supplement for treatment of porphyria. The antioxidant and anti-inflammatory effects of this herb are very effective in treating the symptoms caused due to porphyria.
Why do you think you should go for dietary herbal supplement?
You should go for dietary herbal supplement because:
- Made of natural ingredients.
- Packaged safely in air tight jars.
- Superior quality.
- Offer great value for money.
Here is a list of ingredients used in this dietary herbal supplement for your reference:
- Wattle Bark 116.27mg
- Elephant Creeper 58.11 mg
- Sweet Root 58.13 mg
- Coral Calcium 34.88 mg
- Iron Compound 34.88 mg
- Spanich Chamomile 23.25 mg
- Cloves 23.25 mg
- Vermilion 23.25 mg
- Indian Bay-leaf 23.25 mg
- Nutmeg 23.25 mg
- The herbal pill is intended for oral use only.
- Take 2 tablets each day in the morning after breakfast and evening after dinner.
- Fix times for daily intake and follow precisely.
- Be regular to witness the most results.
Here we have some old school tips compiled for you to take advantage from. We will keep updating them as soon as we come up with something new through experiment. In the meanwhile read and follow these:
- Take average or sometimes high carbohydrate foods.
- Avoid going on crash diets and completely avoid fasting even for a shorter span of time.
- Avoid consuming a lot of milk.
- Take soft liquids that can help regulate bowel movements.
- Avoid iron rich foods.
- Take white bread and anything that is rich in carbohydrates.
- All these tips will keep you motivated and make you feel good about yourself while you are still undergoing the Porphyria management routine with our Herbal Alternative Medicine.
- These tips and tricks are by no means a replacement of actual products.